Pediatric pulmonary lymphatic flow disorders: diagnosis and management

DM Biko, Y Dori, M Savoca, G Krishnamurthy… - Paediatric Respiratory …, 2020 - Elsevier
Pulmonary lymphatic flow disorders involve the abnormal lymphatic flow via lymphatic
channels to the lungs and pleural space. Plastic bronchitis and chylothorax are the main
complications of this abnormal lymphatic perfusion, which has been termed pulmonary
lymphatic perfusion syndrome (PLPS). Following lymphatic access, dynamic contrast MR
lymphangiography is the imaging modality of choice to diagnose these disorders.
Management includes medical therapy, percutaneous interventions under fluoroscopy, and …